02.12.25
AJOMS Volume 2 | Issue 2 ยท Nov 2025 | 101
Hereditary haemorrhagic telangiectasia (HHT) is a vascular disorder that results in the formation of multiple mucocutaneous arteriovenous malformations (AVMs). Clinically, it manifests as telangiectasias resulting in epistaxis, gastrointestinal bleeds and subsequent iron deficiency anaemia, along with visceral AVMs involving the lungs, liver and brain. HHT rarely presents in the oral cavity. It is inherited in an autosomal dominant pattern and commonly presents in the second decade of life with episodes of recurrent epistaxis. This case report outlines a rare presentation of a severe tongue bleed in an individual with HHT in the oral cavity and its management. With oral HHT being uncommon, treatment protocols have not been established.